Gulf Cooperation Counsel Cystic Fibrosis Meeting
February 28th 2007

Plenary

CF FROM GENE TO DISEASE
OBJECTIVES

To describe the genetic background of CF
To learn to understand the relation between different classes of mutations and CFTR function.
To understand the genotype phenotype relation.
To understand the different approach to diagnosis of CF at older age.

PSEUDOMONAS AND THE CF LUNG
OBJECTIVES

To describe the prevalence of chronic Pseudomonas infection in CF
To understand the influence of chronic Pseudomonas infection on lung function and survival.
To understand the difference between normal and epidemic strains of Pseudomonas

ANTIMICROBIAL TREATMENT OF P.AERUGINOSA INFECTIONS
OBJECTIVES

To understand the efficacy of prevention of infection with Pa
To learn the effect of early intervention (eradication) therapy of Pa
To learn the efficacy of inhaled antibiotics
To understand the pharmacodynamics and efficacy of chronic treatment with azithromycin in chronic lung infection with Pa.

NUTRITION AND ENZYMES: THAT’S WHERE IT STARTS!
OBJECTIVES

To highlight the impact of poor nutrition on morbidity and mortality in people with cystic fibrosis
To describe the pathogenesis of malnutrition in cystic fibrosis
To discuss ways to achieve optimal nutrition in people with CF including:
- Diagnosis and treatment of malabsorption
- Early nutritional assessment, intervention and monitoring
To emphasise the importance of a multidisciplinary approach to care

PHYSIOTHERAPY IN CF: STATE OF THE ART
OBJECTIVES

To understand the respiratory patho-physiology from the start, progressing effects on breathing pattern, ventilation distribution, lung volumes and costs of breathing
To highlight the influence of ambition level and treatment goals on treatment approach
To describe conceivable content of modern CF physiotherapy and factors influencing effects of inhalation therapy, choice of airway clearance techniques and allocation of physical exercise
To discuss the different factors influencing and the importance of achieving optimal adherence

WORKSHOPS:

WORKSHOP 1: LUNG INFECTION& TREATMENT
OBJECTIVES
The outcome of this workshop is largely dependent on the cases presented by the participating doctors!!!
Topics that can be discussed:
- infection with S. aureus
- infection with Non Tuberculous microorganisms
- efficacy of nebulisers to be used for inhalation with antibiotics
- treatment of acute infectious exacerbations

WORKSHOP 2: NUTRITION FOR THE NEWBORN WITH CF
OBJECTIVES
To be as interactive as possible
To identify and discuss nutritional problems found in the untreated infant with CF
To identify and discuss methods of achieving optimal nutrition in the newborn
To consider and discuss the introduction of pancreatic enzyme replacement therapy in the newborn
To discuss the management of newborns who require special consideration e.g. those with meconium ileus or failure to thrive

WORKSHOP 3: PHYSIOTHERAPY FOR NEWBORNS AND YOUNG CHILDREN
OBJECTIVES
To discuss current knowledge about apparently asymptomatic infants
To evaluate early symptoms in small children and assessment of therapy
To discuss how to individually tailor adequate treatment for small children
- performance of inhalation therapy in small children, when needed
- airway clearance alternatives in small children, goals
- inclusion of physical exercise from the start
To discuss the family situation as a whole, major responsibility and involvement of siblings in treatment
To discuss family/patient education, adherence with therapy and frequency of follow ups with the physiotherapist

WORKSHOP 4: CF RELATED COMPLICATIONS
OBJECTIVES
Topics that will be discussed
- Non infectious causes of loss in pulmonary function
- Cystic Fibrosis Related Diabetes
- Osteoporosis
- Other issue

WORKSHOP 5: PHYSIOTHERAPY AND EXERCISE IN OLDER PATIENTS
OBJECTIVES
To discuss importance of time- efficient treatment regimens
To highlight benefits of knowing and using the different airway clearance techniques available
To discuss short term and long term evaluation of treatment regimens used
To highlight prevention of musculo-skeletal effects of an obstructive breathing pattern
To discuss effects of patient's role in tailoring every day treatment regimen on adherence
To discuss use of Oxygen supplement
To discuss early use of Non Invasive Ventilation

WORKSHOP 6: Treatment of Malnutrition
OBJECTIVES
To be as interactive as possible
To discuss possible factors that contribute to malnutrition and how these should be assessed
To discuss possible definitions of nutritional failure/malnutrition
To appreciate the need for constant surveillance and monitoring to try and prevent overt malnutrition
To be able to identify appropriate interventions at various stages
To discuss the common forms of nutritional support
To discuss vitamin supplementation

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